Shrinking Lung Syndrome – A rare cause of recurrent dyspnoea in SLE / Hazlyna Baharuddin … [et al.]

Baharuddin, Hazlyna and Mohd Zim, Mohd Arif and Rosman, Azmillah and Mohd Zain, Mollyza (2017) Shrinking Lung Syndrome – A rare cause of recurrent dyspnoea in SLE / Hazlyna Baharuddin … [et al.]. Journal of Clinical and Health Science, 2 (1). pp. 1-4. ISSN 0127 – 984X

Abstract

Here we present a 24-year-old lady with systemic lupus erythematosus (SLE) whom we diagnosed with shrinking lung syndrome (SLS), a rare manifestation of SLE. The initial SLE manifestation was alopecia, thrombocytopenia, serositis and vasculitis. Anti-nuclear antibody (ANA), anti-double stranded DNA (dsDNA) antibody, anti-ribonucleic (RNP) and anti-Ro antibody were positive. A year after diagnosis, she started to develop intermittent dyspnea and was hospitalised on three occasions. Lung examinations revealed reduced breath sounds at both bases and dullness at the right base. Multiple chest radiographs showed bilateral raised hemi-diaphragms. Other investigations including CT pulmonary angiogram, high resolution CT of the thorax, ventilation-perfusion scan and echocardiogram were not significant. On the third hospital admission, we noticed bilateral small lung volumes in the previous high resolution CT scan. Inspiratory and expiratory chest radiographs were performed and showed minimal change in lung volumes and a diagnosis of shrinking lung syndrome (SLS) was made. Her SLE remained active with lupus nephritis despite multiple immunosuppression and she passed away two years later due to sepsis with multi-organ failure.

Metadata

Item Type: Article
Creators:
CreatorsID Num. / Email
Baharuddin, HazlynaUNSPECIFIED
Mohd Zim, Mohd ArifUNSPECIFIED
Rosman, AzmillahUNSPECIFIED
Mohd Zain, MollyzaUNSPECIFIED
Subjects: R Medicine > RC Internal Medicine > Specialties of internal medicine
R Medicine > RC Internal Medicine > Specialties of internal medicine > Diseases of the lungs
Divisions: Universiti Teknologi MARA, Selangor > Puncak Alam Campus > Faculty of Medicine
Journal or Publication Title: Journal of Clinical and Health Science
Journal: UiTM Journal > Journal of Clinical and Health Sciences
ISSN: 0127 – 984X
Volume: 2
Number: 1
Page Range: pp. 1-4
Official URL: https://jchs-medicine.uitm.edu.my/images/manuscrip...
Item ID: 30064
Uncontrolled Keywords: Lupus, small volumes, raised hemi-diaphragms, shrinking lung syndrome, nephritis.
URI: http://ir.uitm.edu.my/id/eprint/30064

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