A Case Of Prader-Willi Syndrome With Behavioural Disturbances: A Successful Multidisciplinary Management Approach / Nor Jannah Nasution Raduan ... [et al.]

Nasution Raduan, Nor Jannah Nasution Raduan and Salleh, Mohd Razali and Bahar, Norharlina and Md Tahir, Mohd Faiz and Md Rosli, Najwa Hanim (2020) A Case Of Prader-Willi Syndrome With Behavioural Disturbances: A Successful Multidisciplinary Management Approach / Nor Jannah Nasution Raduan ... [et al.]. Journal of Clinical and Health Sciences, 5 (1). pp. 83-86. ISSN 0127 – 984X

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Abstract

Prader-Willi Syndrome (PWS) is a genetically determined neurodevelopmental disorder occurring in 1 in 15,000 births. PWS is a rare case in Malaysia and a successful approach to its management has not been well reported here. We present a case of a 13-year-old boy with Prader-Willi Syndrome with prominent behavioural disturbances characterised by temper tantrums, compulsive food intake, stubbornness, stealing and impulsivity further complicated by underlying morbid obesity, poorly controlled type 2 diabetes mellitus, hypertension, dyslipidaemia, obstructive sleep apnoea syndrome and intellectual disability. Multidisciplinary approach involving child and adolescent psychiatrist, occupational therapist, counsellor, family therapist, endocrinologist and dietician has shown to improve the patient’s weight, glucose and blood pressure control and most importantly the behavioural disturbances.

Metadata

Item Type: Article
Creators:
Creators
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Nasution Raduan, Nor Jannah Nasution Raduan
UNSPECIFIED
Salleh, Mohd Razali
UNSPECIFIED
Bahar, Norharlina
UNSPECIFIED
Md Tahir, Mohd Faiz
UNSPECIFIED
Md Rosli, Najwa Hanim
UNSPECIFIED
Subjects: R Medicine > RC Internal Medicine
R Medicine > RJ Pediatrics
R Medicine > RJ Pediatrics > Physiology of children and adolescents
R Medicine > RJ Pediatrics > Diseases of children
Divisions: Universiti Teknologi MARA, Selangor > Puncak Alam Campus > Faculty of Medicine
Journal or Publication Title: Journal of Clinical and Health Sciences
UiTM Journal Collections: UiTM Journal > Journal of Clinical and Health Sciences (JCHS)
ISSN: 0127 – 984X
Volume: 5
Number: 1
Page Range: pp. 83-86
Official URL: https://jchs-medicine.uitm.edu.my/index.php
Item ID: 44156
Uncontrolled Keywords: Prader-Willi Syndrome, adolescent, temper tantrums, behaviour disturbances, intellectual disability
URI: https://ir.uitm.edu.my/id/eprint/44156

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44156

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